Lhermitte-Duclos disease.

Lhermitte-Duclos disease was first described in 1920 in the literature under the names of Purkinjeoma, granular cell hypertrophy of the cerebellum, hamartoma of the cerebellum, dysplastic gangliocytoma, ganglioneuroma, and gangliomatosis of the cerebellum. Patients tend to be young adults and may present with signs of cerebellar dysfunction or increased intracranial pressure secondary to obstructive hydrocephalus. The cerebellar signs are minimal or absent in up to one half of those with the lesion.[1] LDD presents on the MRI as a nonenhancing unilateral lesion in the cerebellum with mass effect on the surrounding structures. The lesion is hypointense on the T1 weighted images and hyperintense on the T2weighted images with alternating parallel hyperintense and isointense stripes which are characteristic of the disease [Figure 2]. These bands correspond to the inner molecular and granular layer of the cerebellum. Loss of central white matter within the folia also contributes to